Hemimacrosomia Syndrome (Steiner Syndrome;
Hemigigantism; Hemifacial or Unilateral
Hypertrophy) 616e48g 616e48g 616e48g 616e48g 616e48g 616e48g 616e48g
General: Occasionally hereditary, although true etiology is obscure; right side affected more frequently than left side; slight male preponderance.
Ocular: Dilated pupil on the affected side; eccentric pupillary location; hypochromic heterochromia.
Clinical: Unilateral facial enlargement may be associated with enlargement of half of entire body to varied extent and degree; thickened skin over involved area with increased activity of sebaceous and sweat glands; telangiectasias and multiple nevi; polydactyly; syndactyly; macrodactyly; scoliosis.
Curtius F. Kongenitaler Partieller Riesenwuchs mit Endokrinen Storungen. Dtsch Arch Klin Med 1925; 147:310.
Geeraets WJ. Ocular Syndromes, 3rd ed. Philadelphia: Lea & Febiger, 1976.
Stafne EC, Lovestedt SA. Congenital hemihypertrophy of the face (facial gigantism). Oral Surg 1962; 15:184.
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