Hunt syndrome (ramsay-hunt syndrome; geniculate neuralgia; herpes zoster auricularis) 5

General: Herpes of the geniculate ganglion; course is prolonged; characterized by severe pain that frequently precedes skin and mucos 818e41i al lesions and may persist for some time after lesions have disappeared; sulfuiduronate enzyme deficiency.

Ocular: Diminished lacrimation; absence of motor corneal reflex on affected side, whereas consensual reflex of noninvolved eye remains normal.

Clinical: Herpes zoster lesions of external ear and oral mucosa; severe pain in area of external auditory meatus and pinna; diminished hearing; tinnitus; vertigo, facial palsy; diminution or total loss of superficial and deep facial reflexes; zoster lesions may involve the scalp, face, and neck; hoarseness; absence of auricular lesions has been reported; progressive dementia; extensive frontal white matter change; myoclonus; ataxia; facial paralysis; tinnitus; hearing loss; hyperacusis; vertigo; dysgeusia; seizures; cerebellar ataxia; schizophrenia-like symptoms.

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Blackley B, et al. Herpes zoster auris associated with facial nerve palsy and auditory nerve symptoms: a case report with histopathological findings. Acta Otolaryngol 1967; 63:533.

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Hori T, et al. Ramsay Hunt syndrome with mental disorder. Jpn J Psychiatry Neurol 199l; 45:873-877.

Hunt JR. On herpetic inflammations of the geniculate ganglion: a new syndrome and its complications. J Nerv Ment Dis N Y 1907; 34:73.

Kobayashi K, et al. Ramsay Hunt syndrome: progressive mental deterioration in association with unusual cerebral white matter change. Clin Neuropathol 1994; 13:88-96.

Shapiro BE, et al. Absence of auricular lesions in Ramsay Hunt syndrome. Neurology 1994; 44:773-774.