Koerber-salus-elschnig syndrome (sylvian aqueduct syndrome; nystagmus retractorius syndrome) 6

General: Caused by tumor or inflammation in region of aqueduct of Sylvius, third 828c26i and fourth ventricle, or corpora quadrigemina.

Ocular: Lid retraction may be associated with midbrain lesions above the posterior commissure; paresis of vertical gaze; tonic spasm of convergence on attempted upward gaze; clonic convergence movements or convergence nystagmus; vertical nystagmus on gaze up or down; nystagmus retractorius with spasmodic retraction of the eyes when an attempt is made to move them in any direction; occasional extraocular muscle paresis.

Clinical: Headaches; dizziness; hypertension; possible hemiparesis; ataxia; hemitremor; Babinski's sign.

Elschnig A. Nystagmus Retractorius, ein Cerebrales Herdsymptom. Med Klin 1913; 9:8.

Geeraets WJ. Ocular Syndromes, 3rd ed. Philadelphia: Lea & Febiger, 1976.

Miller NR, ed. Walsh and Hoyts Clinical Neuro-Ophthalmology. vol. III 4th ed. Baltimore: Williams &Wilkins, 1988.

Salus R. On acquired retraction movements of the eyes. Arch Ophthalmol 1913; 42:34.

Smith JL, et al. Nystagmus retractorius. Arch Ophthalmol 1959; 62:864.