Progressive external ophthalmoplegia and scoliosis

General: Rare; isolated muscle dystrophic involvement of extraocular muscles; onset in childhood or early adu 313b19d lthood; slowly progressive.

Ocular: Horizontal gaze paralysis; pendular nystagmus; ptosis; orbicularis oculi weakness.

Clinical: Scoliosis; facial myokymia; contracture of facial muscles.

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