Schaumann syndrome (besnier-boeck-schaumann syndrome; boeck sarcoid; sarcoidosis) 1

General: Etiology unknown; theories include tuberculosis, hypersensitivity to pine pollen, virus infection; affects blacks most often; c 323i89d hronic course with spontaneous re- missions (see Heerfordt Syndrome); hilar or paratracheal nodes with erythema nodosum known as Lofgren syndrome; onset most often in middle and old age; ocular involvement in 20% to 25% of all cases.

Ocular: Orbital granulomatous mass; bony defects; cutaneous and subcutaneous nodules; myogenic palsy; lacrimal gland adenopathy; decreased tear formation; secondary glaucoma; granulomatous uveitis with iris nodules, cells, and flare; mutton fat keratitic precipitates; keratitis sicca; vitreous floaters; band-shaped keratitis; complicated cataract; inflammatory retinal exudates; 'candle wax drippings'; optic nerve atrophy; neuritis; eyelid nodules; ocular nerve enlargement (granuloma).

Clinical: Lymphadenopathy; hilar nodes; fatigue; cystic, punched-out or reticulated changes in small bones (mainly hands and feet); muscle wasting; contractures; weakness in legs and arms.

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